INTRODUCTION AND OBJECTIVES: An ectopic clitoris is an extremely rare condition which is usually associated with severe defects of the urinary tract. Variances of this anomaly as a bifid clitoris are usually seen in epispadias-extrophy in girls with cloacal anomalies. There are only a few reports of an ectopic clitoris in the current literature.

METHODS: We present the case of an 11 year-old girl who underwent operative correction of anal atresia as a newborn. She was referred to our department for further evaluation because of an unusual appearance of the external genitalia. Clinical examination revealed malposition of the labia minora and absence of a clitoris. On the inner part of the left thigh a structure was seen which could be identified as an ectopic clitoris. X-Ray examination showed a 2 cm diastasis of pubic symphysis. During surgery the ectopic clitoris was completely mobilized and a neurovascular bundle with a single cavernous body was identified. The glans clitoridis and the neurovascular bundle were dissected from the cavernous body and the latter was transsected at the level of the left pubic ramus. Using a subcutaneous tunnel the clitoris was adapted tension free and brought to its correct anatomical position. The impression of the mons pubis was corrected with two overlapping subcutaneous flaps.

RESULTS: Six months postoperatively a very good cosmetic and functional result was achieved.

CONCLUSIONS: We present the successful correction of an extremely rare genital anomaly in a female patient. In evaluating the relevant literature, we did not find a comparable case describing the surgical management.

Source of Funding: none